Etiology
macrophagic activation syndrome
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Blood and immunity
Hematologic disorders
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lymphocytophagocytosis
11 March 2004 -
leukocytes
9 March 2004leucocytes
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dendritic cells
9 March 2004DCs
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T lymphocytes trafficking
9 March 2004T cell migration
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T lymphocytes
9 March 2004T-cells
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X-linked thrombocytopenia
7 March 2004XLT
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thrombocytopenia
7 March 2004 -
multicentric reticulohistiocytosis
6 February 2004Multicentric reticulohistiocytosis is a rare disorder with proliferating histiocytes that develop into multinucleated giant cells with "ground-glass" cytoplasm. The disease presents with a rapidly destructive, sometimes permanently debilitating, polyarthritis and a papulonodular eruption, generally of the face and hands.
Localization
skin
articulations
References
Bogle MA, Tschen JA, Sairam S, McNearney T, Orsak G, Knox JM. Multicentric reticulohistiocytosis with pulmonary (...) -
systemic histiocytoses
6 February 2004Types
Langerhans histiocytosis
non-Langerhans histiocytoses Erdheim-Chester disease systemic juvenile xanthogranuloma generalized eruptive histiocytoma multicentric reticulohistiocytosis (#14639398#, #2192569#) xanthoma disseminatum
References
Weitzman S, Jaffe R. Uncommon histiocytic disorders: the non-Langerhans cell histiocytoses. Pediatr Blood Cancer. 2005 Sep;45(3):256-64. PMID: #15547923#
Jaffe R. The other histiocytosis. Pediatr Dev Pathol. 2004 Jan-Feb;7(1):2-4. PMID: (...) -
reticular dysgenesis
21 January 2004Reticular dysgenesis is a very rare congenital immunodeficiency classified within the severe combined immunodeficiencies (SCID) and characterized by impairment of both lymphoid and myeloid cell development. It is characterized by congenital agranulocytosis, lymphopenia, and lymphoid and thymic hypoplasia with absent cellular and humoral immunity functions. MIM.267500
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