Classification
pigmentary genodermatoses
blistering genodermatoses (heritable skin blistering) Kindler’s syndrome
congenital dyskeratosis
References
Arin MJ, Roop DR. Disease model: heritable skin blistering. Trends Mol Med. 2001 Sep;7(9):422-4. PMID: #11530338#
Home > E. Pathology by systems > Skin
Skin
Adj. cutaneous
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genodermatoses
22 September 2003 -
palmoplantar keratoderma
29 August 2003palmoplantar keratodermas
See also : keratoderma
Etiology
constitutional palmoplantar keratodermas
Unna-Thorst syndrome
Greither’s syndrome
Olmsted’s syndrome
Vohwinkel’s syndrome
Homel-Evans syndrome
Papillon-Lefèevre syndrome
Mal de Maeda
Gamborg Nielsen keratoderma
Huriez’s syndrome (palmoplantar keratoderma with sclerodactyly)
punctate keratoderma
circumscribed keratoderma
Naxos syndrome (MIM.601214) (mutation in the plakoglobin gene MIM.173325)
striate (...) -
epidermal maturation
29 August 2003Anomalies of epidermal maturation and keratinization
ichtyoses
palmoplantar keratodermas
cornoid lamellation
epidermolytic hyperkeratosis
acantholytic dyskeratosis
hypergranolytic dyscornification
colloid keratosis
discrete keratotic lesions
miscellaneous epidermal genodermatoses
granular parakeratosis -
epidermis
29 August 2003Adj. epidermal
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skin
29 August 2003Adj. cutaneous / cutaneous system
Components
epidermis
dermis
cutaneous appendages
sudoral glands
sebaceous glands
hair follicles and hair
hypodermis (subcutis )
Pathology (dermatopathology )
cutaneous developmental anomalies
cutaneous anomalies
cutaneous lesional syndromes
cutaneous diseases
cutaneous tumors
Videos
normal skin by Jerad Gardner
https://youtu.be/yQQ2Dmz42Vs
Thin skin (by Washington Deceit)
http://www.youtube.com/v/-KmfEbKmKFw
Thick skin (...) -
epidermal adhesion
14 July 2003Anomalies of epidermal adhesion
References
Moll R, Moll I. Epidermal adhesion molecules and basement membrane components as target structures of autoimmunity. Virchows Arch. 1998 Jun;432(6):487-504. PMID: #9672190# -
dermatitis
1 July 2003Inflammatory diseases of the skin. dermatitides, Disorders Characterized By Predominant Or Exclusive Dermal Inflammation
Definition: cutaneous inflammation.
CLASSIFICATION:
acute dermatitis
spongiotic dermatitis
interface dermatitis
chronic dermatitis psoriasiform dermatitis eosinophilic dermatitis histiocytic dermatitis granulomatous dermatitis superficial and deep perivascular dermatitis nodular and diffuse infiltrates
cutaneous blistering diseases
vasculitis (...) -
targetoid hemosiderotic hemangioma
23 June 2003hobnail hemangioma ; Hobnail Hemosiderotic Targetoid Hemangioma
Definition: Targetoid hemosiderotic hemangioma is a distinctive, benign vascular tumor.
Images
Hobnail Hemosiderotic Targetoid Hemangioma https://twitter.com/EMadrigalDO/status/869145376032468993
Epidemiology
mostly sporadic
rare familial occurence (#11115185#)
Microscopical synopsis
biphasic growth pattern
dilated vascular structures in the superficial dermis lined by prominent hobnail endothelial cells (...) -
dermatofibrosarcoma protuberans
17 June 2003DFSP
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necrotizing fasciitis
17 June 2003necrotizing acute fasciitis
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