Skin

• incontinentia pigmenti
  18 November 2003

  Incontinentia pigmenti is an uncommon X-linked dominant disorder, lethal in the majority of affected males in utero and variably expressed in females.
  Synopsis
  Cutaneous manifestations 4 stages: vesicular, verrucous, hyperpigmented, and atrophic
  hair anomalies
  nail anomalies
  dental anomalies
  ophthalmologic anomalies
  neurologic deficits
  Etiology
  mutations in the NEMO/IKKgamma gene located at Xq28 NEMO/IKKgamma is an essential component of the nuclear factor kappaB (...)

• dyskeratosis congenita
  18 November 2003

  congenital dyskeratosis, Zinsser-Engman-Cole syndrome
  Definition: Dyskeratosis congenita (DC) is a rare inherited syndrome characterized by the triad of abnormal skin pigmentation, nail dystrophy, mucosal leucoplakia and bone marrow failure syndrome.
  Synopsis
  aplastic anemia
  bone marrow hypoplasia with bone marrow failure and pancytopenia (40%)
  bone marrow failure syndrome
  anemia
  leucopenia
  thrombopenia
  erythrokeratodermia variablis
  chronic keratoconjunctivitis
  nail (...)

• psoriasis
  14 November 2003

  cutaneous psoriasis
  Images
  neutrophils in stratum corneum in psoriasis, vs. pustule of Kogoj in stratum spinosum
  https://twitter.com/DermpathMGH/status/755802030610976768
  Synopsis
  The biopsy shows psoriasis, based on these findings: 1) parakeratosis with 2) an absent granular layer, 3) acanthosis (hyperplasia / overgrowth of the epidermis) most prominent at the rete ridges, 4) dermal chronic inflammation and prominent capillaries.
  Another common finding is 5) neutrophils in the (...)

• hypodermal fat necrosis
  3 November 2003

  post-steroid
  neonatal sclerema

• epidermal tumors
  29 October 2003

  keratinocytic neoplasms, tumors of the epidermis
  Short list
  epidermolytic acanthoma
  wart dyskeratoma
  acantholytic acanthoma
  seborrheic keratosis
  dermatosis papulosa nigra
  melanoacanthoma
  clear cell acanthoma
  clear cell papulosis
  large cell acanthoma
  epidermal dysplasias
  actinic keratosis (solar keratosis )
  actinic cheilitis (solar cheilosis, actinic keratosis of the lip )
  arsenical keratosis
  PUVA keratosis
  intraepidermal carcinoma
  Bowen disease (...)

• epidermal development
  29 October 2003

  epidermal morphogenesis

• congenital self-healing histiocytosis
  24 October 2003

  Immunochemistry
  CD68+
  CD1a- (#1908575#)
  S-100- (#1908575#)
  CD14+ (#1908575#)
  References
  Shy SW, Lee WH, Chang YC, Wu W. A solitary congenital self-healing histiocytosis. Report of a case and review of the literature. Pathol Res Pract. 1996 Aug;192(8):869-74; discussion 875-6. PMID: #8897523#

• cutaneous histiocytoses
  24 October 2003

  primary histiocytic dermatoses, cutaneous histiocytoses, aggressive histiocytic disorders, primary histiocytic dermatoses

• dendrocytes
  24 October 2003

  cutaneous dendrocytes, dermal dendritic cells, dermal dendrocytes

• cytophagic histiocytic panniculitis
  21 October 2003

  Cytophagic histiocytic panniculitis associates with subcutaneous panniculitis associated with hemophagocytic syndrome and is a subcutaneous panniculitic T-cell lymphoma .
  See also
  panniculitis
  histiocytic infiltration cytophagic histiocytic infiltration

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