Kasabach-Merritt syndrome
Definition: Kasabach-Merritt phenomenon (KMP) is characterized by profound thrombocytopenia, microangiopathic hemolytic anemia, a consumptive coagulopathy, and an enlarging vascular lesion.
Kasabach-Merritt phenomenon is a serious coagulopathy associated with kaposiform hemangioendothelioma (KHE), tufted angioma, and possibly other vascular neoplasms.
Classification
vascular tumors
- kaposiform hemangioendothelioma
- tufted angioma
- multifocal lymphangioendotheliomatosis with thrombocytopenia (#15148106#)
- angiosarcoma (#12410374#, #17505172#)
- angioblastoma (#9764180#)
vascular dysplasias
- diffuse splenic hemangiomatosis (#10564388#)
- complex vascular malformations (#12220282#)
fibrosarcoma (#14726860#)