C1 inhibitor deficiency-associated systemic lupus erythematosus
Synopsis
cutaneous lupus
Raynaud phenomenon
non-scarring alopecia
oral ulceration
cerebral vasculitis (#10735963#)
References
Koide M, Shirahama S, Tokura Y, Takigawa M, Hayakawa M, Furukawa F. Lupus erythematosus associated with C1 inhibitor deficiency. J Dermatol. 2002 Aug;29(8):503-7. PMID: #12227484#
Stone NM, Williams A, Wilkinson JD, Bird G. Systemic lupus erythematosus with C1q deficiency. Br J Dermatol. 2000 Mar;142(3):521-4. PMID: #10735963#