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pulmonary sequestration and CPAM association

Definition: Association of an extralobar pulmonary sequestration and a CPAM.

Types

- extralobar sequestration

  • congenital cystic adenomatoid malformation type 2 within a extralobar sequestration (#8516226#)
  • congenital cystic adenomatoid malformation (CCAM or CPAM) connected to an extralobar pulmonary sequestration in the contralateral chest (#15300558#)
  • congenital cystic adenomatoid malformation and extralobar sequestration in the ipsilateral hemithorax (#10663851#)
  • intra-abdominal pulmonary sequestration associated with congenital cystic adenomatoid malformation of the lung (#9587942#, #7944891#)
  • extralobar sequestration, type II congenital cystic adenomatoid malformation, and congenital diaphragmatic hernia (#9025860#)

- intralobar seuestration

  • intralobar pulmonary sequestration with congenital cystic adematous malformation and rhabdomyomatous dysplasia (#14551713#)
  • intralobar pulmonary sequestration with congenital cystic adematous malformation and rhabdomyomatous dysplasia. Pediatr Surg Int. 2003 Oct;19(8):610-1. PMID: #14551713#

References

- McLean SE, Pfeifer JD, Siegel MJ, Jensen ER, Schuler PM, Hirsch R, Mychaliska GB. Congenital cystic adenomatoid malformation connected to an extralobar pulmonary sequestration in the contralateral chest: common origin? J Pediatr Surg. 2004 Aug;39(8):e13-7. PMID: #15300558#

- Orpen N, Goodman R, Bowker C, Lakhoo K. Intralobar pulmonary sequestration with congenital cystic adematous malformation and rhabdomyomatous dysplasia. Pediatr Surg Int. 2003 Oct;19(8):610-1. PMID: #14551713#

- Conran RM, Stocker JT. Extralobar sequestration with frequently associated congenital cystic adenomatoid malformation, type 2: report of 50 cases. Pediatr Dev Pathol. 1999 Sep-Oct;2(5):454-63. PMID: #10441623#

See also

- pulmonary malformations