Home > D. Systemic pathology > Hematopathology > transient abnormal myelopoiesis
transient abnormal myelopoiesis
Wednesday 8 November 2006
Synopsis
severe fetal liver failure (15202167)
hepatomegaly
tumor lysis syndrome (16970788)
hepatic fibrosis (liver fibrosis) (16440800, 8537505)
multiple organ failure (12107683)
isolated pericardial effusion (11049242)
monoclonality of proliferating cells (1672097)
congenital hemochromatosis (1836197)
Etiology
trisomy 21 (15202167, 17804520, 17437323)
Noonan syndrome (12468921)
References
Shiozawa Y, Fujita H, Fujimura J, Suzuki K, Sato H, Saito M, Shimizu T, Yamashiro Y. A fetal case of transient abnormal myelopoiesis with severe liver failure in Down syndrome: prognostic value of serum markers. Pediatr Hematol Oncol. 2004 Apr-May;21(3):273-8. PMID: 15202167
Silvio F, Carlo L, Elena B, Nicoletta B, Daniela F, Roberto M. Transient abnormal myelopoiesis in Noonan syndrome. J Pediatr Hematol Oncol. 2002 Dec;24(9):763-4. PMID: 12468921