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sporadic visceral myopathy with inclusion bodies
Monday 13 February 2006
Synopsis
chronic intestinal pseudo-obstruction
primary visceral myopathy
fibrosis of the muscularis externa
vacuolar degeneration of myocytes
leiomyocytic cytoplasmic inclusions
- numerous inclusions
- greatly enhanced by PAS staining
- inclusions present in both muscularis externae and muscularis mucosae
- identified in mucosal biopsy specimens
Ultrastructure
myofibrils at various stages of degeneration
See also
visceral myopathies
References
Fogel SP, DeTar MW, Shimada H, Chandrasoma PT. Sporadic visceral myopathy with inclusion bodies. A light-microscopic and ultrastructural study. Am J Surg Pathol. 1993 May;17(5):473-81. PMID: 8385883