Home > D. Systemic pathology > Genetic and developmental anomalies > generalized peeling skin syndrome
generalized peeling skin syndrome
Monday 6 February 2012
Definition: Generalized peeling skin syndrome (PSS) is an autosomal recessive genodermatosis characterized by lifelong, continuous shedding of the upper epidermis.
Etiology
mutation in the CHST8 gene in autosomal recessive peeling skin syndrome. (22289416)