Humpath.com - Human pathology - Photos - pictures - videos

neurenteric cyst

A neurenteric cyst of the spine is a rare congenital disorder secondary to alimentary duplication and vertebral malformation.

It should be included in the differential diagnosis of an intradural, extramedullary spinal lesion.

Localization

- cervical neurenteric cyst
- abdominal neurenteric cyst

Associations

- Klippel-Feil syndrome (#1764851#)
- hydrocephalus

  • aqueductal stenosis

- vertebral segmentation anomalies
- fused costae
- anal atresia
- renal dysplasia
- bicornuate uterus
- double blind vagina
- transdiaphragmatic duodenal duplication (#15108090#)

References

- Giant transdiaphragmatic duodenal duplication with an intraspinal neurenteric cyst as part of the split notochord syndrome: report of a case. Wakisaka M, Nakada K, Kitagawa H, Shimada H, Nosaka S. Surg Today. 2004;34(5):459-62. PMID: #15108090#

- Orstavik KH, Steen-Johnsen J, Foerster A, Fjeld T, Skullerud K, Lie SO. VACTERL or MURCS association in a girl with neurenteric cyst and identical thoracic malformations in the father: a case of gonosomal mosaicism? Am J Med Genet. 1992 Aug 1;43(6):1035-8. PMID: #1415331#

- Neurenteric cysts—a spectrum. Alrabeeah A, Gillis DA, Giacomantonio M, Lau H. J Pediatr Surg. 1988 Aug;23(8):752-4. PMID: #3171846#