pediatric fibrous tumors
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[ (||image_reduire{0,60}|inserer_attribut{alt,Fibrous hamartoma of infancy (juvenile fibrous hamartoma)}) ]Classification
reactive lesions
- hypertrophic scars
- keloid
Benign neoplasms
- acrochordon (skin tag, soft fibroma)
- dermatomyofibroma
- storiform collagenoma (sclerotic fibroma)
- solitary myofibroma
- giant cell fibroblastoma
- fibroma of tendon sheath
- infantile digital fibromatosis (inclusion body fibromatosis)
- calcifying aponeurotic fibroma
- knuckle pad
- acquired digital fibrokeratoma
- infantile myofibromatosis
- fibrous hamartoma of infancy
- juvenile hyalin fibromatosis
- nodular fasciitis
- proliferative myositis
- elastofibroma
- fibrous hamartoma
- infantile digital fibroma
- sclerosing perineurioma
Locally aggressive fibrous lesions
- palmar fibromatosis
- plantar fibromatosis
- penile fibromatosis
- desmoid fibromatosis
Low-grade malignant lesions
- dermatofibrosarcoma protuberans
Malignant lesions
- ETV6-NTRK3+ infantile fibrosarcoma
- adult-type fibrosarcoma
Features
hyaline cytoplasmic globules -> juvenile digital fibroma
EMA+ epithelioid cells -> sclerosing perineurioma
See also
Tumors
- fibrous tumors
- cutaneous fibrous tumors
- deep fibrous tumors
References
Mehregan AH. Superficial fibrous tumors in childhood.
J Cutan Pathol. 1981 Oct;8(5):321-34. PMID: #7037883#
Keasbey LE. Juvenile aponeurotic fibroma (calcifying fibroma); a distinctive tumor arising in the palms and soles of young children. Cancer. 1953 Mar;6(2):338-46. PMID: #13032926#