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pediatric fibrous tumors

Classification

- reactive lesions

  • hypertrophic scars
  • keloid

- Benign neoplasms

  • acrochordon (skin tag, soft fibroma)
  • dermatomyofibroma
  • storiform collagenoma (sclerotic fibroma)
  • solitary myofibroma
  • giant cell fibroblastoma
  • fibroma of tendon sheath
  • infantile digital fibromatosis (inclusion body fibromatosis)
  • calcifying aponeurotic fibroma
  • knuckle pad
  • acquired digital fibrokeratoma
  • infantile myofibromatosis
  • fibrous hamartoma of infancy
  • juvenile hyalin fibromatosis
  • nodular fasciitis
  • proliferative myositis
  • elastofibroma
  • fibrous hamartoma
  • infantile digital fibroma
  • sclerosing perineurioma

- Locally aggressive fibrous lesions

  • palmar fibromatosis
  • plantar fibromatosis
  • penile fibromatosis
  • desmoid fibromatosis

- Low-grade malignant lesions

  • dermatofibrosarcoma protuberans

- Malignant lesions

  • ETV6-NTRK3+ infantile fibrosarcoma
  • adult-type fibrosarcoma

Features

- hyaline cytoplasmic globules -> juvenile digital fibroma
- EMA+ epithelioid cells -> sclerosing perineurioma

See also

- Tumors

  • fibrous tumors
    • cutaneous fibrous tumors
    • deep fibrous tumors

References

- Mehregan AH. Superficial fibrous tumors in childhood. J Cutan Pathol. 1981 Oct;8(5):321-34. PMID: #7037883#

- Keasbey LE. Juvenile aponeurotic fibroma (calcifying fibroma); a distinctive tumor arising in the palms and soles of young children. Cancer. 1953 Mar;6(2):338-46. PMID: #13032926#