hepatic Zellweger syndrome
Zellweger disease is the most severe of the peroxisome biogenesis disorders. The peroxisome biogenesis disorders are subdivided into 12 complementation groups (CGs).
Synopsis
absent liver peroxisomes
intrahepatic biliary dysgenesis
prolonged neonatal jaundice
See also
peroxisomal diseases
- Zellweger disease