Humpath.com - Human pathology

Home > B. Cellular pathology > polyglucosan bodies

polyglucosan bodies

Tuesday 3 January 2006

Types

 Lafora bodies
 Lafora body-like inclusions
 Bielschowsky bodies
 GSD4 type polyglucosan bodies

Etiology (polyglucosan diseases)

 Lafora bodies

  • Lafora disease

 Lafora body-like inclusions

  • Disulfiram treatment

 glycogen storage disease type 4 (GSD4)
 adult polyglucosan body disease (APBD) (MIM.263570)

See also

 cellular inclusions

  • cytoplasmic inclusions

References

 Congenital type IV glycogenosis: the spectrum of pleomorphic polyglucosan bodies in muscle, nerve, and spinal cord with two novel mutations in the GBE1 gene. Nolte KW, Janecke AR, Vorgerd M, Weis J, Schröder JM. Acta Neuropathol. 2008 Nov;116(5):491-506. PMID: 18661138