autoimmune enteric leiomyositis
Autoimmune enteric leiomyositis (AIELM) is an extraordinary rare cause of acquired chronic intestinal pseudo-obstruction in children.
Synopsis
acquired chronic intestinal pseudoobstruction (acquired CIPO)
dense lymphocytic infiltrate of the muscularis propria
- mainly consisting of cytotoxic T lymphocytes
smooth muscle fibers degenerated and diminished
myenteric plexus intact
mucosa and submucosa without severe inflammatory changes
Associations
autoimmune hepatitis
gastritis
colitis
See also
enteric leiomyositis
References
Haas S, Bindl L, Fischer HP. Autoimmune enteric leiomyositis: a rare cause of chronic intestinal pseudo-obstruction with specific morphological features. Hum Pathol. 2005 May;36(5):576-80. PMID: #15948126#
Ruuska TH, Karikoski R, Smith VV, et al. Acquired myopathic intestinal pseudo-obstruction may be due to autoimmune enteric leiomyositis. Gastroenterology 2002; 122:1133-1139.