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meconial ileus

Definition: digestive meconial obstruction.

Meconium ileus (MI) is defined as the intraluminal inspissation of protein-rich viscid meconium in the small intestine, is the most common gastrointestinal manifestation of cystic fibrosis.

MI can be simple or complicated by volvulus or ischemia of the dilated proximal ileal segment with subsequent intestinal necrosis, jejunoileal atresia or ileal perforation with meconium peritonitis.

Etiology

- viscous meconium

  • cystic fibrosis (mucoviscidosis)

- fetal achylia(#14267605#)

  • fetal pancreatic fibrosis (#7304173#)
    • association bilateral renal dysplasia, fetal pancreatic fibrosis, meconium ileus, and situs inversus totalis (#7304173#)

- pancreatic aplasia (pancreas agenesis) (#7949819#, #5774443#)

Association

- neonatal hemochromatosis (#11700892#)

Complications

- digestive atresia
- digestive stenosis
- digestive perforation
- digestive volvulus (neonatal volvulus)

Videos

- Meconium obstruction with necrosis

See also

- meconial plug