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COL7A1

MIM.120120 3p21.3

Pathology

- gerline mutations in:

  • autosomal recessive epidermolysis bullosa dystrophica (MIM.226600)
  • autosomal dominant epidermolysis bullosa dystrophica (MIM.131750)
  • pretibial epidermolysis bullosa (MIM.131850)
  • mild form of localized recessive epidermolysis bullosa dystrophica (MIM.226600)
  • transient bullous dermolysis of the newborn (TBDN) (MIM.131705)
  • autosomal dominant epidermolysis bullosa pruriginosa (MIM.604129)
  • autosomal recessive epidermolysis bullosa pruriginosa (MIM.604129)
  • isolated nail dystrophy (MIM.607523)