Home > E. Pathology by systems > Digestive system > Small intestine > intestinal lymphangiectasia
intestinal lymphangiectasia
Monday 7 July 2003
Ent. Waldman, 1961
Images
Small intestine polyp. Secondary Lymphangiectasia
Synopsis
loss of chylous fluid into the gut lumen
chylous ascite, chylous pleural effusions
protein-losing enteropathy syndrome
- lymphopenia
- hypogammaglobulinaemia
Etiology
primitive intestinal lymphangiectasia (congenital obstructive defects of the digestive lymphatics) (Waldmann disease)
primitive intestinal lymphangiectasia in other genetic diseases
- aplasia cutis (MIM.207731)
- Hennekam lymphangiectasia (MIM.235510)
secondary intestinal lymphagiectasia
- lymph node obstruction
- acute inflammation
- infectious enteritis
- intestinal fibrosis
- intraluminal precipitates
- extraluminal compression
- lymph node infiltration
- increased thoracic duct pressure
- constrictive pericarditis
- right heart disease
- cardiomyopathy
- carcinoid syndrome
- atrial septal defect
- pulmonary stenosis
- Behcet disease
- post-Fontan operation (1785336)
See also
- digestive lymphatic anomalies