glutaminolysis
Pathology
activating regulatory mutations of glutamate dehydrogenase (GDH) in congenital hyperinsulinism with hyperammonemia (GDH-HI or HI/HA
References
Kelly A, Li C, Gao Z, Stanley CA, Matschinsky FM. Glutaminolysis and insulin secretion: from bedside to bench and back. Diabetes. 2002 Dec;51 Suppl 3:S421-6. PMID: #12475785#