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systemic granulomatoses

Tuesday 10 June 2003

Etiology:

 infectious systemic granulomatoses

  • tuberculosis
  • atypical mycobacteriosis
    • Mycobacterium kansasii
    • Mycobacterium avium intracellualre (MAI)

 systemic tuberculoid granulomatoses

 systemic necrotizing granulomatosis
 Wegener granulomatosis
 Churg-Strauss angiitis

 tumoral systemic granulomatoses

  • lymphomatoid granulomatosis
  • T-cell lymphomas

 systemic histiocytoses

  • langerhans histiocytosis
  • non-Langerhans cell histiocytoses
    • Erdheim-Chester disease
    • systemic juvenile xanthogranuloma
    • necrobiotic xanthogranuloma
    • adult disseminated xanthoma

 constitutional immune deficiencies

 miscellaneous

  • lipogranulomatoses
  • hyalinizing plasmacytic granulomatosis (2451439)
  • familial juvenile systemic granulomatosis (FJSG)

Localization

 tracheal granulomatosis
 pulmonary granulomatosis

  • bronchocentric granulomatosis
  • bronchiolocentric granulomatosis

 renal granulomatosis
 splenic granulomatosis
 digestive granulomatosis

Types

 necrotizing granulomatosis
 tuberculoid granulomatosis (sarcoid granulomatosis)
 familial systemic granulomatosis

See also

 Granulomas

  • tuberculoid granuloma
    • epithelioid granuloma

References

 Schuetz C, Huck K, Gudowius S, Megahed M, Feyen O, Hubner B, Schneider DT, Manfras B, Pannicke U, Willemze R, Knüchel R, Göbel U, Schulz A, Borkhardt A, Friedrich W, Schwarz K, Niehues T. An immunodeficiency disease with RAG mutations and granulomas. N Engl J Med. 2008 May 8;358(19):2030-8. PMID: 18463379


 Atlas of Granulomatous Diseases by Yale Rosen, M.D.

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