Home > E. Pathology by systems > Digestive system > chronic intestinal pseudo-obstruction
chronic intestinal pseudo-obstruction
Monday 9 June 2003
Lesions
Etiology
genetic chronic intestinal pseudo-obstruction
- SOX10-associated chronic intestinal pseudo-obstruction
- FLNA (filamin-A) mutations in X-linked chronic idiopathic intestinal pseudo-obstruction with central nervous system involvement (17357080)
infectious
- Chagas enteropathy
dysimmunity
- slcerodermy
- systemic lupus erythematosus (10981652, 10713642, 9771415, 8474080)
- autoantibodies against proliferating cell nuclear antigen (8639186)
See also
colonic dysmotility
References
Gargiulo A, Auricchio R, Barone MV, Cotugno G, Reardon W, Milla PJ, Ballabio A, Ciccodicola A, Auricchio A. Filamin A is mutated in X-linked chronic idiopathic intestinal pseudo-obstruction with central nervous system involvement. Am J Hum Genet. 2007 Apr;80(4):751-8. PMID: 17357080
Park SH, Min H, Chi JG, Park KW, Yang HR, Seo JK. Immunohistochemical studies of pediatric intestinal pseudo-obstruction: bcl2, a valuable biomarker to detect immature enteric ganglion cells. Am J Surg Pathol. 2005 Aug;29(8):1017-24. PMID: 16006795
Streutker CJ, Huizinga JD, Campbell F, Ho J, Riddell RH. Loss of CD117 (c-kit)- and CD34-positive ICC and associated CD34-positive fibroblasts defines a subpopulation of chronic intestinal pseudo-obstruction. Am J Surg Pathol. 2003 Feb;27(2):228-35. PMID: 12548170
Hirano I, Pandolfino J. Chronic intestinal pseudo-obstruction. Dig Dis. 2000;18(2):83-92. PMID: 11060471