pulmonary Hurler disease
Lung in Hurler disease; lung involvement in Hurler disease, Alpha-L-Iduronidase Deficiency, IDUA Deficiency, MPS I. Includes: Hurler Syndrome (MPS I H), Hurler-Scheie Syndrome (MPS I H/S), Scheie Syndrome (MPS I S)
Digital case
Case 202 (HPC:202) : Lung in Hurler disease
Synopsis
interstitial pneumonia
interstitial deposition of mucopolysaccharides
cholesterol bronchiolitis
See also
Hurler disease
References