Humpath.com - Human pathology

Home > D. General pathology > Genetic and developmental anomalies > Chromosomal diseases > Microdeletion syndromes > del(13)(q32q33.2) deletion syndrome

del(13)(q32q33.2) deletion syndrome

Saturday 30 October 2010

Synopsis

 fish mouth
 choanal atresia
 severe mental
 motor retardation

Cytogenetics

 del(13)(q32q33.2)

Nota bene: 13q deletion syndrome is characterized by mental and motor retardation, craniofacial dysmorphic facial appearance and various congenital malformations.

References

 Partial deletion of the long arm of chromosome 13 (q32q33.2) associated with mental retardation, choanal atresia and fish mouth. Balci S, Yuksel Konuk B, Atik F, Oguz AK, Ergun MA, Baltaci V, Kosyakova N, Liehr T. Genet Couns. 2010;21(3):317-24. PMID: 20964123