Home > E. Pathology by systems > Digestive system > Small intestine > intestinal leiomyositis
intestinal leiomyositis
Friday 23 October 2009
Synopsis
chronic intestinal pseudo-obstruction (CIP)
Association
eosinophilic fasciitis
decreased diffusion capacity
Microscopy
inflammatory myopathy
dense lymphoid infiltrate
extensive loss of the muscularis propria layers
Treatment
immunosuppressive therapy with cyclosporin
Etiology
autoimmune enteric leiomyositis (15948126)
See also
digestive myopathies
digestive neuropathies
References
Chronic intestinal pseudo-obstruction caused by an intestinal inflammatory myopathy: case report and review of the literature. Dewit S, de Hertogh G, Geboes K, Tack J. Neurogastroenterol Motil. 2008 Apr;20(4):343-8. PMID: 18004985
Haas S, Bindl L, Fischer HP. Autoimmune enteric leiomyositis: a rare cause of chronic intestinal pseudo-obstruction with specific morphological features. Hum Pathol. 2005 May;36(5):576-80. PMID: 15948126