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fibrous tumors

Digital cases

- Case 219 : Desmoid fibromatosis
- UI:868 - Abdominal desmoid fibromatosis

Definition: A fibrous tumor is a tumor that elaborate a significant amount of collagen. Fibroous tumors often contain numerous fibroblastic or myofibroblastic cells (fibroblastic tumors/myofibroblastic tumors

Types

- cutaneous fibrous tumors (superficial fibrous tumors)
- deep fibrous tumors

Classification

- Reactive lesions

  • hypertrophic scars
  • keloid

- Benign neoplasms

  • acrochordon (skin tag, soft fibroma)
  • storiform collagenoma (sclerotic fibroma)
  • myofibroblastic tumors
    • dermatomyofibroma
    • solitary myofibroma
    • infantile myofibromatosis
  • giant cell fibroblastoma
  • fibromas
    • fibroma of tendon sheath
    • calcifying aponeurotic fibroma
  • infantile digital fibromatosis (inclusion body fibromatosis)
  • knuckle pad
  • Acquired digital fibrokeratoma
  • fibrous hamartoma of infancy
  • juvenile hyalin fibromatosis
  • nodular fasciitis
  • proliferative myositis
  • elastofibroma
  • fibrous hamartoma
  • infantile digital fibroma
  • sclerosing perineurioma

- benign fibrous histiocytofibroma (dermatofibroma)

- Locally aggressive fibrous lesions

  • palmar fibromatosis
  • plantar fibromatosis
  • penile fibromatosis
  • desmoid fibromatosis (desmoid fibromas)

- Low-grade malignant lesions

  • dermatofibrosarcoma protuberans

- Malignant lesions

  • ETV6-NTRK3+ infantile fibrosarcoma
  • adult-type fibrosarcoma

See also

- sclerosing tumors
- fibroblastic tumors
- myofibroblastic tumors