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C1ORF36

MIM.180040 1q32.3

The retinopathy-associated RD3 protein could be part of subnuclear protein complexes involved in diverse processes, such as transcription and splicing.

Pathology

- germline mutations of C1ORF36 in retinal degeneration or Leber congenital amaurosis locus 12 (LCA12) (MIM.610612)

Animal model

The rd3 mouse is one of the oldest identified models of early-onset retinal degeneration.

References

- Friedman JS, Chang B, Kannabiran C, Chakarova C, Singh HP, Jalali S, Hawes NL, Branham K, Othman M, Filippova E, Thompson DA, Webster AR, AndrĂ©asson S, Jacobson SG, Bhattacharya SS, Heckenlively JR, Swaroop A. Premature truncation of a novel protein, RD3, exhibiting subnuclear localization is associated with retinal degeneration. Am J Hum Genet. 2006 Dec;79(6):1059-70. PMID: #17186464#