congenital pulmonary lymphangiectasis
Types
CPL, Noonan Group 1
CPL, Noonan Group 2
CPL, Noonan Group 3
unilobar congenital pulmonary lymphangiectasis (UCPL) (#15136998#)
Associations
Ivemark syndrome with asplenia
- total anomalous pulmonary venous connection (TAPVC)
- atrioventricular communis
- septal defects
cardiovascular malformations
- total anomalous pulmonary venous connection (TAPVC)
- aortic arch malformation
- hypoplastic left heart (left heart hypoplasia)
- atrioventricular communis
- ventricular septal defect (VSD)
congenital lobar emphysema (#4715376#, #5936105#)
renal malformations
ichtyosis congenita
cystic fibrosis
generalized lymphangioma
omphalocele (exomphalos)
See also
pulmonary lymphangiectases
References
Congenital pulmonary lymphangiectasis: report of an autopsy case masquerading as pulmonary interstitial emphysema. Yamada S, Hisaoka M, Hamada T, Araki S, Shiraishi M. Pathol Res Pract. 2010 Jul 15;206(7):522-6. PMID: #20399027#
Chapdelaine J, Beaunoyer M, St-Vil D, Oligny LL, Garel L, Bütter A, Di Lorenzo M. Unilobar congenital pulmonary lymphangiectasis mimicking congenital lobar emphysema: an underestimated presentation? J Pediatr Surg. 2004 May;39(5):677-80. PMID: #15136998#