right atrial isomerism
Definition: Isomerism of the right atrial appendages is caracterized by bilateral morphologically right atrial appendages with mirror-imaged of cardiac atria. It is associated with complex congenital cardiac lesions and ciliary abnormalities.
Associations
complex cardiac malformations
- anomalies of pulmonary venous return +/- pulmonary venous obstruction
asplenia
bronchial ciliary anomalies
- narrow, disorganized bronchial epithelium
- abundant goblet cells
- short, angulated cilia with a random orientation
- abnormal central microtubule doublet
See also
isomerisms
- cardiac isomerism
- pulmonary isomerism
- visceral isomerism
primary ciliary dyskinesia (PCD) and ciliary anomalies
- immotile cilia syndrome
- Kartagener syndrome
random lateralization
- mirror-imaged arrangement of the organs
- isomeric patterns
polysplenia or asplenia
bronchial isomerisms
- left bronchial isomerism
- right bronchial isomerism
visceroatrial situs inversus
References
Raman R, Al-Ali SY, Poole CA, Dawson BV, Carman JB, Calder L. Isomerism of the right atrial appendages: clinical, anatomical, and microscopic study of a long-surviving case with asplenia and ciliary abnormalities. Clin Anat. 2003 May;16(3):269-76. PMID: #12673825#