osseous Rosai-Dorfman disease
Sinus histiocytosis with massive lymphadenopathy or Rosai-Dorfman disease (RDD) is a rare histiocytic proliferative disorder of unknown etiology.
Most patients present with lymph node involvement manifesting as adenopathy; however, RDD may arise primarily in a variety of extranodal sites, including bone.
See also
Rosai-Dorfman disease
References
Primary Rosai-Dorfman Disease of Bone: A Clinicopathologic Study of 15 Cases. Demicco EG, Rosenberg AE, Björnsson J, Rybak LD, Unni KK, Nielsen GP. Am J Surg Pathol. 2010 Sep;34(9):1324-33. PMID: #20679880#
Extranodal Rosai-Dorfman disease with multifocal bone and epidural involvement causing recurrent spinal cord compression. Al-Saad K, Thorner P, Ngan BY, Gerstle JT, Kulkarni AV, Babyn P, Grant RM, Read S, Laxer RM, Chan HS. Pediatr Dev Pathol. 2005 Sep-Oct;8(5):593-8. PMID: #16211443#