Home > E. Pathology by systems > Skin > nevus lipomatosus superficialis
nevus lipomatosus superficialis
Thursday 12 January 2006
naevus lipomatosus superficialis ; nevus lipomatosus cutaneous superficialis, Hoffmann-Zurhelle
WKP | PO |
Definition: Nevus lipomatosus superficialis (NLS) is a rare benign cutaneous hamartoma characterized by papules and nodules usually in the pelvic and sacral areas, with ectopic mature adipose tissue reaching the superficial dermis.
Images
nevus lipomatosus superficialis
- macroscopical : https://twitter.com/JAADjournals/status/1194333303609925633
- https://twitter.com/sumskindoc/status/725872399506366464
- https://twitter.com/luishcruzc/status/1248302310775816192
- https://twitter.com/drsys02/status/720639038525415424
Synopsis
Rare, benign cutaneous hamartoma
@<@ 2y
Multiple soft, papules, nodules, plaques
Buttocks, upper thigh, lower back
Normal epidermis
Superficial dermis with lobules of adipocytes
Associations
multiple folliculosebaceous cystic hamartomas (FCH) (15649197)
dermoid cysts (15649197)
perifollicular fibrosis (14721781)
basal cell carcinoma (12786865)
cavernous hemangioma (3074101)
Cytogenetics
2p24 deletion (17223884)
See also
Skin
- cutaneous anomalies
- cutaneous tumors
References
Cardot-Leccia N, Italiano A, Monteil MC, Basc E, Perrin C, Pedeutour F. Naevus lipomatosus superficialis: a case report with a 2p24 deletion. Br J Dermatol. 2007 Feb;156(2):380-1. PMID: 17223884