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cardiac rhabdomyoma

Thursday 11 November 2004

myocardial rhabdomyoma

Images

 cardiac rhabdomyoma: Spider cells : Large polygonal cells with glycogen vacuoles

Digital slides

 Case 49 (HPC:49)
 Case 64 (HPC:64)

Synopsis

 spider-shaped rhabdomyocytes (spider cells)

Predisposition

 tuberous sclerosis (MIM.191100)

  • TSC1 (MIM.605284) at 9q34
  • TSC2 (MIM.191092) at 16p13.3
  • TSC3 at 12q14 (MIM.191091)
  • TSC4 (MIM.191090)

See also

 cardiac tumors
 rhabdomyomas