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lymphangiomyomatosis

Tuesday 13 July 2004

Localization

 pulmonary lymphangiomyomatosis
 thoracic lymphangiomyomatosis
 abdominal lymphangiomyomatosis
 retroperitoneal lymphangiomyomatosis
 uterine lymphangiomyomatosis

Predisposition

 tuberous sclerosis

Molecular biology

 TSC1 and TSC2 mutations

  • in tuberous sclerosis associated lymphangiomyomatosis
  • in sporadic lymphangiomyomatosis (11829138)

See also

 lymphangiomyoma