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fibromatoses

Monday 1 March 2004

Digital case

 JRC:11438 : Superficial fibromatosis (Juvenile, digital) (NOS)

Definition: Fibromatoses are rare soft tissue disease characterized by fibroblastic proliferation.

Classification

 fibroblastic fibromatoses

  • desmoid fibromatosis (desmoid tumor, aggressive fibromatosis)
  • fibromatosis colli
  • digital infantile fibromatosis
  • aponevrotic fibromatosis
    • plantar fibromatosis
    • palmar fibromatosis
    • penile fibromatosis
  • hereditary gingival fibromatosis (idiopathic gingival fibromatosis)
  • lipofibromatosis

 myofibroblastic fibromatoses (myofibromatoses)

According to the localization

 superficial fibromatoses
 deep fibromatoses

See also

 fibrous tumors
 fibroblastic tumors

References

 Montgomery E, Lee JH, Abraham SC, Wu TT. Superficial fibromatoses are genetically distinct from deep fibromatoses. Mod Pathol 2001 Jul;14(7):695-701

 Allen PW. The fibromatoses: a clinicopathologic classification based on 140 cases. Am J Surg Pathol. 1977 Sep;1(3):255-70.