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adrenal leiomyosarcoma

Sunday 18 March 2018

Definition : Primary adrenal leiomyosarcoma is a exceedingly rare adrenal tumor thought to be originated from smooth muscle wall of central adrenal vein. SMA and desmin IHC is diffusely positive.

Differential diagnosis

 sarcomatoid adrenal cortical carcinoma
 malignant PEComa
 dedifferentiated liposarcoma
 adrenal metastasis

Images

 primary adrenal leiomyosarcoma

See also

 adrenal tumors
 leiomyosarcoma / leiomyosarcomas