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micronodular pneumocyte hyperplasia
Tuesday 29 August 2017
First recognized in 1991 by HH Popper (Histopathology 1991;18:347). Also called, multifocal micronodular pneumocyte hyperplasia (MMPH); acinar atypical adenomatoid proliferation of epithelium, multiple adenomatoid lesions, micronodular hyperplasia of type II pneumocytes.
Definition : MPH is a benign, hamartomatous, multinodular proliferation of type II pneumocytes. It is often associated with tuberous sclerosis complex and may coexist with lymphangioleiomyomatosis (LAM).