Humpath.com - Human pathology

Home > E. Pathology by systems > Digestive system > Small intestine > pneumatosis cystoides intestinalis

pneumatosis cystoides intestinalis

Tuesday 17 May 2016

PO

Image

 pneumatosis cystoides intestinalis

Synopsis

 submucosal gas filled cysts within gastrointestinal tract
 empty submucosal cysts lined by multinucleated giant cells
 Mucosa may demonstrate cryptitis , crypt abscesses , granulomas
 Can also resemble digestive parietla lipomatosis

Associations

 In infants, fulminant form is associated with necrotizing enterocolitis and may be fatal
 Also associated with cystic fibrosis or congenital heart defects
 In adults, either idiopathic or associated with :

  • digestive obstruction ,
  • chronic lung disease ,
  • scleroderma ,
  • chemotherapy ,
  • drugs ,
  • ischemic colitis ,
  • vascular insufficiency or
  • infection with gas producing bacteria, such as Clostridia

Differential diagnosis

 lipomatosis

Complications

 bowel necrosis
 perforation
 peritonitis

See also

 pneumatosis

  • pneumatosis intestinalis