Home > E. Pathology by systems > Digestive system > Small intestine > pneumatosis cystoides intestinalis
pneumatosis cystoides intestinalis
Tuesday 17 May 2016
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pneumatosis cystoides intestinalis
Synopsis
submucosal gas filled cysts within gastrointestinal tract
empty submucosal cysts lined by multinucleated giant cells
Mucosa may demonstrate cryptitis , crypt abscesses , granulomas
Can also resemble digestive parietla lipomatosis
Associations
In infants, fulminant form is associated with necrotizing enterocolitis and may be fatal
Also associated with cystic fibrosis or congenital heart defects
In adults, either idiopathic or associated with :
- digestive obstruction ,
- chronic lung disease ,
- scleroderma ,
- chemotherapy ,
- drugs ,
- ischemic colitis ,
- vascular insufficiency or
- infection with gas producing bacteria, such as Clostridia
Differential diagnosis
lipomatosis
Complications
bowel necrosis
perforation
peritonitis
See also
pneumatosis
- pneumatosis intestinalis