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dural angioleiomyoma
Friday 23 March 2012
Angioleiomyomas of the Dura
Angioleiomyomas (ALMs) are cutaneous and soft tissue lesions usually seen in the lower extremities of middle-aged women.
The lesions are nodular, mulberry like, and composed of vessels of varying size with abundant intervening smooth muscle; an arterial component is absent.
Intracranial examples are exceedingly rare, with @<@10 cases reported to date, and are usually dural in location.
Dural ALMs are easily clinically mistaken for CCMs or meningiomas but are not of similar histopathogenesis.
References
Angioleiomyomas of the Dura: Rare Entities That Lack KRIT1 Mutations. Conner TM, Waziri A, Kleinschmidt-Demasters BK. Am J Surg Pathol. 2012 Apr;36(4):526-33. PMID: 22261708