Home > D. General pathology > Blood and immunity > IgA plasmacytoma
IgA plasmacytoma
Tuesday 30 November 2010
Definition: plasmacytomas expressing immunoglobulin A.
Localization
nodal IgA plasmacytoma
extranodal IgA plasmacytoma
Types
IgA plasmacytoma
Plasmacytomas expressing immunoglobulin A are rare and not well characterized. Nodal and extranodal plasmacytomas expressing immunoglobulin A are an indolent lymphoproliferative disorder with a low risk of clinical progression.
IgA plasmacytomas may represent a distinct form of extramedullary plasmacytoma characterized by younger age at presentation, frequent lymph node involvement, and low risk of progression to plasma cell myeloma. (20871216)
References
Nodal and extranodal plasmacytomas expressing immunoglobulin A: an indolent lymphoproliferative disorder with a low risk of clinical progression. Shao H, Xi L, Raffeld M, Pittaluga S, Dunleavy K, Wilson WH, Spector N, Milito C, Morais JC, Jaffe ES. Am J Surg Pathol. 2010 Oct;34(10):1425-35.PMID: 20871216