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Sjögren disease
Wednesday 24 March 2010
primary Sjögren’s syndrome; Goujerot-Sjögren disease; Sjögren syndrome
Sjogren’s syndrome causes keratoconjunctivitis sicca and xerostomia. It can also cause other exocrine abnormalities such as vaginal dryness, bronchitis, and affect other organs.
Anti-SS-A (Ro) and anti-SS-B (La) antibodies
Anti-SS-A(Ro) antibodies are found in many autoimmune disorders, such as SLE, subacute cutaneous lupus, neonatal lupus, ANA negative lupus, Sjogren’s syndrome, primary biliary cirrhosis, chronic active hepatitis, and rheumatoid arthritis.
Anti-SS-B (La) is far more specific for Sjogren’s syndrome than anti-SSA. It is also found in SLE.
Digital case
HPC:309 : Salivary gland in Sjögren syndrome
Synopsis
pulmonary Sjögren disease
- interstitial lung diseases (ILDs)
- usual interstitial pneumonia (UIP)
- non-specific interstitial pneumonia (NSIP)
- lymphocytic interstitial pneumonia (LIP)
- bronchiolitis obliterans and organising pneumonia (BOOP)
- lymphoproliferative disorders of the lung
- lymphocytic interstitial pneumonia (LIP)
- follicular bronchiolitis
- pulmonary nodular lymphoid hyperplasia (PNLH)
- low-grade lymphomas
salivary Sjögren disease
References