congenital iris ectropion

Congenital iris ectropion is a rare, usually nonprogressive anomaly characterized by the posterior iris pigment epithelium on the anterior surface of the iris stroma, anterior insertion of the iris root, and trabecular dysgenesis.

It is frequently associated with developmental glaucoma and may occur as part of a systemic disorder including neurofibromatosis, primary facial hemihypertrophy, Rieger anomaly, and Prader-Willi syndrome.

Associations

 neurofibromatosis
 primary facial hemihypertrophy
 Rieger anomaly
 Prader-Willi syndrome
 intestinal neuronal dysplasia