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mammary sarcomas
Thursday 5 July 2012
Definition : Primary breast sarcoma (PBS) is a rare and heterogeneous group.
Breast sarcoma, excluding phyllodes tumor, is an extremely rare and heterogeneous group of malignancies, constituting less than 1% of total breast malignancies and less than 5% of all soft tissue sarcomas (STS)1.
It can be divided into two categories:
de novo development (primary)
or therapy-related development (secondary).
Although clinical features of primary breast sarcoma (PBS) mimic mammary adenocarcinoma in some ways, it conveys a high risk of recurrence and carries a significantly worse prognosis.
Types (examples)
mammary fibrosarcoma
angiosarcoma
Digital cases
JRC:5320 : mammary fibrosarcoma.
JRC:5321 : mammary fibrosarcoma.
JRC:5322 : mammary fibrosarcoma.
JRC:5406 : mammary sarcoma (Metastatic to lung).
JRC:5392 : mammary osteosarcoma (in a dog).
See also
mammary tumors
sarcomas
Open references
Breast sarcoma – a review of diagnosis and management. 2009. PDF
https://ac.els-cdn.com/S1743919108001854/1-s2.0-S1743919108001854-main.pdf?_tid=65c08701-50eb-4cc5-afac-ef4f373e5e4a&acdnat;=1546167081_7b7689fe496b5c5e6b54ed3b99df412b
Primary female breast sarcoma: clinicopathological features, treatment and prognosis. 2016
https://www.ncbi.nlm.nih.gov/pmc/articles/PMC4980597/