fibrolipomatous hamartoma

Predisposition

 tuberous sclerosis

• Tuberous sclerosis is a rare congenital disorder with an incidence of 1 in 6000 births.
• The classic triad is seizure, mental deficiency, and angiofibromas.
• Orofacial manifestations include fibrous hyperplasia, hemangioma, bifid uvula, cleft lip and palate, macroglossia, high arched palate, and enamel defects.
• Benign tumors of the jaws including desmoplastic fibroma, calcifying odontogenic tumor, and odontogenic myxoma have been recently reported in tuberous sclerosis.

References

 Fibrolipomatous hamartoma in a patient with tuberous sclerosis: report of a case. Celenk P, Alkan A, Canger EM, Günhan O. Oral Surg Oral Med Oral Pathol Oral Radiol Endod. 2005 Feb;99(2):202-6. PMID: 15660093